Objective:

To explore the CT

MRI and PET/CT imaging features of adult alveolar soft part sarcoma (ASPS).

Methods:

The clinical data

CT

MRI and PET/CT imaging features of ten patients with histopathologically proved ASPS from January 2012 to December 2016 were retrospectively reviewed.

Results:

The median age of the ten patients was 29 years (22-46 years). The median size of the lesions was 72 mm (29-260 mm). Seven lesions were in the extremities (4 cases in the thigh)

and 3 cases in the pelvic. Tumors were hyper-intensity on T1WI and heterogeneous hyper-intensity or mixed hypo-/hyper-intensity on T2WI. All lesions sh

owed marked heterogeneous enhancement and numerous large vessels on both contrast-enhanced T1WI and contrast-enhanced CT. All primary lesions and most of metastases were fluorodeoxyglucose (FDG)-avid on PET/CT. And metastases developed in 9 cases (9 cases in lungs

3 cases in lymph nodes

2 cases in bones

1 case in subcutaneous tissues and 1 case in brain).

Conclusion:

Adult ASPS predominantly develops in the extremities of young patients. Tumors show hyper-intensity on T1WI

and marked heterogeneous enhancement and numerous large vessels on both contrast-enhanced T1WI and contrast-enhanced CT. Pulmonary metastasis develops in the majority of ASPS patients.